医学
呼吸窘迫
间质性肺病
羟基氯喹
内科学
队列
疾病
复合杂合度
表型
儿科
肺
肿瘤科
外科
基因
遗传学
传染病(医学专业)
生物
2019年冠状病毒病(COVID-19)
作者
Carolin Kröner,Thomas Wittmann,Simone Reu,Veronika Teusch,Mathias Klemme,Daniela Rauch,Meike Hengst,Matthias Kappler,Nazan Çobanoğlu,Tuğba Şişmanlar Eyüboğlu,Ayşe Tana Aslan,Ilaria Campo,Marijke Proesmans,T Schaible,Susanne Terheggen-Lagro,Nicolas Regamey,Ernst Eber,Jürgen Seidenberg,Nicolaus Schwerk,Charalampos Aslanidis
出处
期刊:Thorax
[BMJ]
日期:2016-08-11
卷期号:72 (3): 213-220
被引量:145
标识
DOI:10.1136/thoraxjnl-2016-208649
摘要
Overall long-term (>5 years) survival of subjects with two disease-causing ABCA3 mutations was <20%. Response to therapies needs to be ascertained in randomised controlled trials.
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