Gynadroblastoma is an extremely rare tumour of the ovary containing both a granulosa cell and a Sertoli-Leydig cell tumour. We report a case of gynandroblastoma of the right ovary Stage IA (FIGO) in a 15-year-old girl. Microscopically, the tumour composed predominantly of granulosa cells with a minoritary component, although more than 10%, of Sertoli cells. The present knowledge about its nature, function and behaviour are reviewed.