Progress in the diagnosis and treatment of Kartagener syndrome in children

Kartagener syndrome is a rare autosomal recessive disease with low incidence.Clinically, typical visceral inversion, bronchiectasis and sinusitis triad are typical.The pathogenesis of the disease is not clear.The principle of treatment is mainly symptomatic treatment, postponing the progress of bronchiectasis, Lack of fundamental treatment.The disease generally has a good prognosis.This article reviews recent advances in the diagnosis and treatment of Kartagener syndrome at home and abroad. Key words: Kartagener syndrome; Primary ciliary dyskinesia; Children; Gene; Cilia