Surgical management of a low-birth-weight neonate with ductal-dependent pulmonary circulation

The present investigation was approved by the institutional review board of the authors’ hospital. Given the observational nature of the study, requirements for informed written consent were waived (IRB-2009-023; approval, October 23, 2020). A 10-day-old girl weighing 1998 g at birth with right atrial isomerism, functional single ventricle, pulmonary atresia, bilateral superior venous cava, patent ductus arteriosus (PDA), right aortic arch, infracardiac total anomalous pulmonary venous connection (TAPVC), and patent ductus venosus (DV) underwent a Fontan repair procedure after several palliations (Figures 1 and 2).