Pulmonary capillary hemangiomatosis (PCH) is a rare pulmonary vascular disorder with a prevalence of approximately 4 cases per million individuals. It is characterized by pulmonary hypertension leading to symptoms of shortness of breath and dyspnea, and rarely hemoptysis or chest pain. This manuscript reported a case of PCH that was initially misdiagnosed as hypersensitive pneumonitis and was finally confirmed by thoracoscopic lung biopsy. The aim of this report was to increase diagnostic awareness and improve the management of this disease.