Prosthetic Rehabilitation Of An Adult Patient With Hypohidrotic Ectodermal Dysplasia: A Clinical Report

Ectodermal dysplasia (ED) comprises a large, heterogeneous group of inherited disorders that are defined by primary defects in the development of two or more tissues derived from embryonic ectoderm. The tissues primarily involved are the skin, hair, nails, eccrine glands, and teeth. The ectodermal dysplasias are congenital, diffuse, and nonprogressive. To date, more than 192 distinct disorders have been described. The most common ectodermal dysplasias are X-linked recessive hypohidrotic ectodermal dysplasia (Christ-Siemens-Touraine syndrome)1,2 and hidrotic ectodermal dysplasia (Clouston syndrome)3. This case report emphasizes on the prosthetic management of ectodermal dysplasia by enhancing the appearance and function through individual Porcelain fused to metal crowns and interim removable partial denture.