MR of diabetes insipidus in a patient with Erdheim-Chester disease: case report.

Twenty-six cases of Erdheim-Chester disease have been reported since it was first described in 1930. CNS involvement is highly unusual. In their review of 19 cases of the disease, Miller et al. found only one instance of central diabetes insipidus and hypopituitarism. We report a rare case of neurogenic diabetes insipidus associated with Erdheim-Chester disease