Objective:To discuss diagnosis and treatment of duplicated kidney complicated with hydronephrosis.Methods: Clinical data of 7 cases of duplicated kidney complicated with hydronephrosis were analysed retrospectively.The group has 2 male and 5 female cases,who are 35~71 years old.Results: 3 cases complicated with serious hydronephrosis underwent partial nephrectomy and relieved after 1~3 years follow-up;4 cases complicated with mild hydronephrosis received no additional treatments and their hydrops were not obvious increased after 3 months~1 year follow-up.Conclusions: For diagnosis of duplicated kidney complicated with hydronephrosis,intravenous urography usually is sufficient,but it is difficult to identify duplicated kidney complicated with serious hydronephrosis and large renal cyst by intravenous urography,since the duplicated renal pelvis and calyces are not develop or underdeveloped.For these cases,CT(CTU) examination was helpful for diagnosis.The duplicated kidney complicated with mild hydronephrosis patients can receive no additional treatments with observation and follow-up,but the patients with serious hydronephrosis should undergo partial nephrectomy.For atypical renal cyst,a careful exploration for bottom of cyst cavity in operation is helpful to prevent misdiagnosing duplicated kidney complicated with hydronephrosis as large renal cyst.