桥粒蛋白
医学
心脏病学
内科学
心肌病
心肌炎
心动过速
烧蚀
心力衰竭
病理生理学
射频消融术
细胞
遗传学
生物
作者
Stephan A C Schoonvelde,Frank R.N. van Schaagen,Alexander Hirsch,Michelle Michels,Sing‐Chien Yap
标识
DOI:10.1016/j.hrcr.2024.04.005
摘要
Desmoplakin (DSP) cardiomyopathy is an inherited left-dominant arrhythmogenic cardiomyopathy associated with heart failure, epicardial ventricular fibrosis, and ventricular arrhythmias (VA). Inflammation may play a potential role in its pathophysiology given that myocarditis-like episodes ("hot-phase
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