Dermatofibrosarcoma protuberans recurrence: Size matters

Have you managed patients with dermatofibrosarcoma protuberans (DFSP)? Probably more often than the literature suggests. DFSP presents as an indurated plaque with raised violaceous to red-brown nodules, occurring most often in the third to fifth decade of life. The pigmented variant of DFSP (Bednar tumor) and the fibrosarcomatous variant, account for <5% and up to 15% of cases, respectively. Lesions can reach several centimeters in diameter. Lesions may ulcerate and become painful. Most DFSPs occur on the trunk (50%), extremities (35%), and head and neck (15%).