objective:To analyze the clinical manifestation,diagnosis,mis-diagnostic reasons and treatment method of orbital NK/T cell lymphoma.Methods:The literature was reviewed and 2 patients with orbital NK/T cell lymphoma were collected.Then we analyzed the diagnosis,differential diagnosis and therapy of orbital N K/T cell lymphoma.Results:Orbital NK/T cell lymphoma was one kind of relatively rare,new reported extra-nodal lymphoma,which was usually mis-diagnosed as conjunctivitis,idiopathic orbital inflammation,periorbital area inflammation.The orbital NK/T cell lymphoma and nasal NK/T cell lymphoma shared similar stopathology,immunopathology.Conclusions:The orbital NK/T cell lymphoma shows distinctive cliniopathologic,immunophenotypic and characteristic CT or MRI manifestations.The patients are diagnosed difficultly in the early stage,presented highly aggressive clinic course and a very high lethality.