Ebstein anomaly: A personalized approach to symptomatic neonates

The severely symptomatic neonate with Ebstein anomaly (EA) of the tricuspid valve continues to be the Achilles heel of pediatric cardiac surgery, with hospital mortality remaining the greatest of any surgical procedure, including the Norwood operation.1,2 In the early 1990s, Starnes and colleagues3 reported a new single-ventricle palliation, and Knott-Craig and colleagues4 reported a new biventricular repair, both with hospital survival of approximately 80%. In this Featured Case, we present our most recent experience with 3 consecutive critically ill neonates with EA, each with a different presentation.