Calcinosis cutis is a term used to describe a group of disorders in which calcium deposits form in the skin and classified as metastatic, dystrophic, idiopathic and iatrogenic. The present case has calcinosis cutis with features of Raynaud’s phenomenon, oesophageal dysmotility, sclerodactyly and telangiectasia (CREST syndrome) the patients with CREST syndrome often have better prognosis than diffuse systemic sclerosis. Hence pathologist should be aware that localized calcium deposition in dermis may be associated with systemic collagen vascular disease.