Immunoglobulin M (IgM) multiple myeloma is a very rare hematologic malignancy which comprises less than only 0.5% of multiple myeloma (MM) cases.Immunoglobulin M multiple myeloma and Waldenstrom's macroglobulinemia (WM) are two distinct hematologic entities with the common finding of IgM monoclonal gammopathy.This article presents a case of IgM multiple myeloma with increased monoclonal IgM overlapping with multiple myeloma.