Nevus sebaceous associated with basal cell carcinoma

Nevus sebaceous of Jadassohn is a congenital, uncommon hamartomatous lesion of the epidermis, dermis, and appendages with the predominance of sebaceous elements. This hamartoma has the capacity to develop benign as well as malignant neoplasms, but the malignant transformation is rare. Herein, we report a case of basal cell carcinoma in the background of nevus sebaceous in a 53-year-old female highlighting the importance of prophylactic excision of this lesion.