医学
自身免疫性胰腺炎
IgG4相关疾病
恶性肿瘤
病理
腹膜后纤维化
神秘的
间质性肺病
胰腺炎
胰腺
放射科
肺
疾病
胃肠病学
纤维化
内科学
替代医学
作者
Madhuri Shimpi Mahajan,Sudeshna Maitra,Natasha Singh,Melvika Pereira
出处
期刊:DOAJ: Directory of Open Access Journals - DOAJ
日期:2017-07-27
卷期号:27 (2): 249-253
被引量:1
标识
DOI:10.4103/ijri.ijri_135_16
摘要
Immunoglobulin G4 (IgG4)-related systemic disease (IgG4-RSD) is a new systemic entity associated with autoimmune pancreatitis (AIP). Other organ involvements take the form of sclerosing cholangitis, sclerosing cholecystitis, sclerosing sialadenitis, retroperitoneal fibrosis, and interstitial nephritis. Recently, lung diseases related to IgG4 have been described to occur with or without other organ involvement. These diseases include interstitial lung disease (ILD), pulmonary inflammatory pseudotumor, and lymphomatoid granulomatosis. Most of these cases occur in combination with AIP, which also appears to have a general preponderance for males. The true incidence of IgG4-related ILD and the incidence of AIP are unknown. Here, we describe a case of a 53-year-old gentleman who presented with weight loss, fever, loose motions, altered sensorium, and persistent low hemoglobin, for which he was referred for 18-fluorodeoxyglucose positron emission tomography/computed tomography scan to diagnose probable underlying occult malignancy/paraneoplastic syndrome. It revealed features suggestive of IgG4 disease involving the pancreas and lungs, which was confirmed subsequently.
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