医学
内科学
急性白血病
肿瘤科
儿科
梅德林
临床试验
急性淋巴细胞白血病
疾病
白血病
重症监护医学
表型
年轻人
作者
Hannah Goulart,Farhad Ravandi,Nicholas J. Short,Nitin Jain,Naval Daver,Tapan M. Kadia,Courtney D. DiNardo,Gautam Borthakur,Koichi Takahashi,Naveen Pemmaraju,Fadi Haddad,Guillermo Montalban‐Bravo,Yesid Alvarado,Ghayas C. Issa,Álex Bataller,Sherry Pierce,Sanam Loghavi,Guilin Tang,Sa A. Wang,Beenu Thakral
摘要
PURPOSE Mixed phenotype acute leukemia (MPAL) is a rare clinical entity with historically poor outcomes. METHODS We conducted a retrospective analysis of adults 18 years and older with newly diagnosed B-cell (B/M) or T-cell/myeloid (T/M) MPAL treated at our institution between 2017 and 2024. RESULTS We identified 42 patients (median age 70 years); 20 (48%) had B/M MPAL, and 22 (52%) had T/M MPAL; 57% of patients had adverse risk cytogenetics, and 41% had a TP53 mutation. Sixty-two percent of patients were treated with a hybrid regimen, and 45% of patients received intensive therapy. A composite complete remission (CRc; CR + CRi) was achieved in 57% of patients (86% measurable residual disease [MRD]–negative). After a median follow-up of 27.9 months, the median relapse-free survival in patients achieving an overall response (CRc + morphological leukemia-free state) was 10.1 months, 17.8 months in those who achieved a CRc, and not reached (NR) in patients with MRD-negative CRc. The median overall survival (OS) for all patients was 9.5 months and NR for patients achieving a CRc. Although patients with T/M MPAL had a trend toward improved survival compared with those with B/M MPAL (median OS of 9.1 v 25 months P = .28), this difference abrogated when comparison was stratified by treatment intensity. Twelve patients (29%) underwent allogeneic hematopoietic stem-cell transplantation (HSCT); on landmark analysis, HSCT trended to improve OS (NR v 22.8, P = .12). Multivariate Cox analysis demonstrated that TP53 mutation was associated with increased hazards for death (hazard ratio [HR], 3.5, P = .01), whereas the use of intensive chemotherapy trended to be favorable (HR, 0.45, P = .11). CONCLUSION Overall, these data demonstrate the need for treatment intensification in MPAL with HSCT in first remission for best outcomes.
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