Carotid-Cavernous Fistula Treatment in Vascular Ehlers-Danlos Syndrome: A Case Report and Review of Management

HomeStrokeVol. 54, No. 8Carotid-Cavernous Fistula Treatment in Vascular Ehlers-Danlos Syndrome: A Case Report and Review of Management No AccessCase ReportRequest AccessFull TextAboutView Full TextView PDFView EPUBSections ToolsAdd to favoritesDownload citationsTrack citationsPermissions ShareShare onFacebookTwitterLinked InMendeleyReddit Jump toNo AccessCase ReportRequest AccessFull TextCarotid-Cavernous Fistula Treatment in Vascular Ehlers-Danlos Syndrome: A Case Report and Review of Management Gregory J. Wong, Arjun V. Pendharkar, Kyle A. Lyman, Prateek Thatikunta, Lironn D. Kraler, Christina Mijalski, David H. Liang and Robert L. Dodd Gregory J. WongGregory J. Wong Correspondence to: Gregory J. Wong, MD, Department of Neurology & Neurological Sciences, Stanford University, 453 Quarry Rd, Stanford, CA 94305. Email E-mail Address: [email protected] https://orcid.org/0000-0002-7544-2140 Department of Neurology & Neurological Sciences (G.J.W., K.A.L., P.T., L.D.K., C.M.), Stanford University, Palo Alto, CA. , Arjun V. PendharkarArjun V. Pendharkar Department of Neurosurgery (A.V.P., R.L.D.), Stanford University, Palo Alto, CA. Division of Interventional Neuroradiology, Department of Radiology (A.V.P., R.L.D.), Stanford University, Palo Alto, CA. , Kyle A. LymanKyle A. Lyman https://orcid.org/0000-0002-3309-7211 Department of Neurology & Neurological Sciences (G.J.W., K.A.L., P.T., L.D.K., C.M.), Stanford University, Palo Alto, CA. , Prateek ThatikuntaPrateek Thatikunta https://orcid.org/0000-0001-6542-2827 Department of Neurology & Neurological Sciences (G.J.W., K.A.L., P.T., L.D.K., C.M.), Stanford University, Palo Alto, CA. , Lironn D. KralerLironn D. Kraler Department of Neurology & Neurological Sciences (G.J.W., K.A.L., P.T., L.D.K., C.M.), Stanford University, Palo Alto, CA. , Christina MijalskiChristina Mijalski https://orcid.org/0000-0002-9199-7322 Department of Neurology & Neurological Sciences (G.J.W., K.A.L., P.T., L.D.K., C.M.), Stanford University, Palo Alto, CA. , David H. LiangDavid H. Liang Division of Cardiovascular Medicine (D.H.L.), Stanford University, Palo Alto, CA. and Robert L. DoddRobert L. Dodd https://orcid.org/0000-0001-5609-9474 Department of Neurosurgery (A.V.P., R.L.D.), Stanford University, Palo Alto, CA. Division of Interventional Neuroradiology, Department of Radiology (A.V.P., R.L.D.), Stanford University, Palo Alto, CA. Originally published25 May 2023https://doi.org/10.1161/STROKEAHA.123.042623Stroke. 2023;54:e403–e406FootnotesFor Sources of Funding and Disclosures, see page e406.Correspondence to: Gregory J. Wong, MD, Department of Neurology & Neurological Sciences, Stanford University, 453 Quarry Rd, Stanford, CA 94305. Email gjwong@stanford.eduREFERENCES1. Adham S, Trystram D, Albuisson J, Domigo V, Legrand A, Jeunemaitre X, Frank M. Pathophysiology of carotid-cavernous fistulas in vascular Ehlers-Danlos syndrome: a retrospective cohort and comprehensive review.Orphanet J Rare Dis. 2018; 13:100. doi: 10.1186/s13023-018-0842-2CrossrefGoogle Scholar2. Pepin M, Schwarze U, Superti-Furga A, Byers PH. Clinical and genetic features of Ehlers–Danlos syndrome Type IV, the vascular type.New Engl J Med. 2000; 342:673–680. doi: 10.1056/NEJM200003093421001CrossrefMedlineGoogle Scholar3. Khan A, Chaudhary N, Pandey AS, Gemmete JJ. Direct puncture of the highest cervical segment of the internal carotid artery for treatment of an iatrogenic carotid cavernous fistula in a patient with Ehlers-Danlos syndrome.J Neurointerv Surg. 2012; 4:e29. doi: 10.1136/neurintsurg-2011-010075CrossrefGoogle Scholar4. 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Comments are not published in an issue and are not indexed in PubMed. Comments should be no longer than 500 words and will only be posted online. References are limited to 10. Authors of the article cited in the comment will be invited to reply, as appropriate.Comments and feedback on AHA/ASA Scientific Statements and Guidelines should be directed to the AHA/ASA Manuscript Oversight Committee via its Correspondence page.Sign In to Submit a Response to This Article Previous Back to top Next FiguresReferencesRelatedDetails August 2023Vol 54, Issue 8 Advertisement Article InformationMetrics © 2023 American Heart Association, Inc.https://doi.org/10.1161/STROKEAHA.123.042623PMID: 37226776 Originally publishedMay 25, 2023 Keywordsaneurysmscarotid arterycarotid-cavernous sinus fistulasEhlers-Danlos Syndrometype IVPDF download Advertisement SubjectsCerebrovascular Procedures