Inflammatory Myofibroblastic Tumor of the Orbit Presenting as a Subconjunctival Mass

PURPOSE: To present a case of inflammatory myofibroblastic tumor in the anterior orbit and to describe its clinical features, diagnosis, and management. METHODS: Case report and literature review. RESULTS: A 10-year-old boy presented with diplopia and limited ocular motility in his right eye secondary to a subconjunctival mass in the right supranasal side. Incisional biopsy and debulking were performed. Histopathologic examination showed the proliferation of spindle-shaped myofibroblasts that were immunoreactive for smooth muscle actin and vimentin and infiltrate of inflammatory cells. CONCLUSIONS: We believe this is the first case of an inflammatory myofibroblastic tumor found localized in the orbit.