原发性硬化性胆管炎
自身免疫性胰腺炎
医学
胃肠病学
内科学
胰腺炎
病理
疾病
标识
DOI:10.1097/mcg.0000000000001984
摘要
IgG4-related sclerosing cholangitis (IgG4-SC) is a unique, steroid-responsive, fibroinflammatory condition that is more commonly found in older men and is strongly associated with autoimmune pancreatitis (AIP). It may pose a diagnostic challenge at times due to closely mimicking hepatobiliary diseases such as primary sclerosing cholangitis (PSC), secondary sclerosing cholangitis (SSC), and cholangiocarcinoma. IgG4-SC has an excellent prognosis when promptly diagnosed and treated with steroids. Literature search strategy: The authors searched PubMed and Google Scholar, for articles with the search terms “autoimmune cholangiopathy” and “IgG4 cholangiopathy.”
科研通智能强力驱动
Strongly Powered by AbleSci AI