医学
溶血
胎儿血红蛋白
血红蛋白
贫血
镰状细胞性贫血
溶血性贫血
病理生理学
血红蛋白病
胎儿
血管闭塞
疾病
免疫学
怀孕
内科学
遗传学
生物
摘要
Sickle hemoglobin polymerizes when it is deoxygenated, thereby damaging the sickle erythrocyte and initiating vascular occlusion and hemolysis. Preventing the polymerization of sickle hemoglobin should avert the secondary pathophysiological consequences of polymerization-induced vaso-occlusion and hemolytic anemia; it is a preferred approach to disease-modifying treatment1 (
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