Pediatric Choroidal Coloboma with Macular Hole at the Edge of the Coloboma

A 10-year-old girl with best-corrected visual acuity (BCVA) of 20/60 in the right eye. Right fundus showed type 3 choroidal coloboma (CC) with a full-thickness macular hole (MH) at its temporal edge, and left eye had type 1 CC (Ida Mann classification: type 1, coloboma extending above disc; type 2, superior border of disc; type 3, separated from lower border of disc by normal retina; type 4, inferior crescent below disc; type 5, isolated gap in the line of fissure; type 6, area of pigmentary disturbance; type 7, extreme peripheral coloboma). Swept-source optical coherence tomography shows MH with cystic changes in the retina overlying non-colobomatous area and a rudimentary intercalary membrane extending beyond the hole over the coloboma (Fig 1, the yellow arrow indicates the macular hole at the edge of the coloboma; and the white arrow indicates the intercalary membrane overlying the coloboma).