Aortopulmonary Collateral Arteries in Noncyanotic Congenital Heart Disease

Development of major aortopulmonary collateral arteries (MAPCAs) are strongly associated with cyanotic congenital heart disease. However, MAPCAs have rarely been reported in non-cyanotic congenital heart disease. We report on a rare case of a newborn originally diagnosed with an atrial septal defect, a ventricular septal defect, and pulmonary arterial hypertension, who underwent complete repair. Failure to progress postoperatively, lead to the delayed diagnosis of aortopulmonary collateral arteries (APC's). Percutaneous embolization and surgical ligation of APC's resulted in rapid recovery.