医学
贲门失弛缓症
巨结肠
巨结肠病
疾病
外科
胃肠病学
内科学
食管
作者
Roshni Dasgupta,Jacob C. Langer
标识
DOI:10.1097/01.mpg.0000304448.69305.28
摘要
Hirschsprung disease occurs approximately once in every 5000 live-born infants. It is characterized by the absence of ganglion cells in the myenteric and submucosal plexuses of the intestine. Once the diagnosis of Hirschsprung disease has been made, most patients are now treated with a transanal approach to resection. We review the early and late postoperative complications. Late complications include persistent mechanical obstruction, recurrent or acquired aganglionosis, disordered motility in the proximal colon or small bowel, internal sphincter achalasia, or functional megacolon caused by stool-holding behavior. These children require complex interdisciplinary care to ensure an adequate quality of life.
科研通智能强力驱动
Strongly Powered by AbleSci AI