DEGOS’S DISEASE: FROM A BENIGN FORM TO A MALIGNANT COURSE

Degos disease or atrophic papulosis is a rare chronic occlusive vasculopathy with an unknown pathogenesis. To date the disease is divided into a benign long-term skin form and a malignant systemic form with damage to the organs of the gastrointestinal tract and central nervous system, which is accompanied by a high risk of death. The described clinical case of a man with a benign cutaneous form of Degos disease demonstrates a rare variant of the disease with erosive and ulcerative lesions of the penis. The skin process on the trunk and extremities is represented by typical pale pink papules with atrophic scars in the center as well as erosions and ulcers on the skin of the penis. During the follow-up, the patient developed thrombosis and gangrene of the small intestine, which may indicate the development of a systemic disease and malignancy of Degos disease. We continue to monitor the patient.