Advances of treatment of pulmonary atresia with intact ventricular septum

Pulmonary atresia with intact ventricular septum(PA/IVS) is a rare, critical and complicated cyanotic congenital heart disease, the natural mortality rate is high, if not treated, 50% of newborns died within 2 weeks after birth, about 85% of newborns will die within six months. In recent years, with cardiac surgery procedures, catheter intervention and other treatment levels improved, the survival rate of newborns after surgery has improved. Over the past decade, the disease 5-year survival rate increased by 75% or more . In this paper, PA/IVS cardiac surgery procedures, catheter intervention and hybrid treatment were reviewed, aimed at providing a reference for clinical treatment.