A 21-year-old woman was seen at the hospital because of lower abdominal pain. A soft mass was palpable with the fingertip on the posterior wall of the rectum. CT, magnetic resonance imaging and transrectal ultrasonographic examination showed a presacral cystic tumor. The tumor was resected by using a sacral approach. Histological examination showed that the tumor wall was made of squamous epithelium without any adnexal structure, and hence it was diagnosed as epidermoid cyst. In a review of the Japanese literature, 31 cases of presacral epidermoid cyst are seen. Complete excision of those presacral cysts is advised because of possible complications including infection and malignancy.